The anaesthetic management of temporal tumour resection in a patient with type 1 glutaric aciduria Tip-1 glutarik asidürisi olan temporal tümör rezeksiyonu uygulanan bir hastada anestezi deneyimimiz


Dilmen Ö. K., Akçil E. F., TUNALI Y., Tütüncü A. Ç., Utku T., ERBABACAN Ş. E., ...Daha Fazla

Turk Anesteziyoloji ve Reanimasyon Dernegi Dergisi, cilt.41, sa.4, ss.139-141, 2013 (Scopus, TRDizin) identifier

Özet

Glutaric aciduria type 1 (GA-1) is an uncommon cerebral organic aciduria. The risk of acute encephalopathic crises and metabolic acidosis may present during anaesthetic and surgical or postsurgical periods. Few cases with GA-1 who underwent general anaesthesia have been reported previously, and there are no data on long-term anaesthetic management of patients with GA-1. We report the anaesthetic management of temporal tumour resection that lasted for 8 hours in a 16-year-old patient with GA-1, and discuss the risks of malignant hyperthermia and propofol infusion syndrome. © 2013 by Turkish Anaesthesiology and Intensive Care Society.