Case Report of a Patient With Malignant Peripheral Nerve Sheath Tumor Treated With Wide Resection


Celayir A., Özer M., Kavak Ş., Özşahin M. K., Botanlıoğlu H.

CUREUS, cilt.15, sa.11, ss.1-2, 2023 (ESCI)

  • Yayın Türü: Makale / Vaka Takdimi
  • Cilt numarası: 15 Sayı: 11
  • Basım Tarihi: 2023
  • Doi Numarası: 10.7759/cureus.49055
  • Dergi Adı: CUREUS
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI)
  • Sayfa Sayıları: ss.1-2
  • İstanbul Üniversitesi-Cerrahpaşa Adresli: Evet

Özet

Malignant peripheral nerve sheath tumors are soft tissue sarcomas originating from peripheral nerves. They are more frequently diagnosed in individuals with neurofibromatosis and tend to affect young men more often than women. The most common sites for these tumors within the peripheral nerve sheath are in the pelvis and the distal femur.

Although chemotherapy and radiotherapy are not frequently used, it should be noted that in some cases, postoperative radiotherapy and chemotherapy may be beneficial. The primary treatment approach typically involves the complete surgical removal of the tumor. Here, we discuss the case of our patient whom we successfully treated with extensive resection and followed up with postoperative radiotherapy at our clinic.

Malignant peripheral nerve sheath tumors are soft tissue sarcomas originating from peripheral nerves. They are more frequently diagnosed in individuals with neurofibromatosis and tend to affect young men more often than women. The most common sites for these tumors within the peripheral nerve sheath are in the pelvis and the distal femur.

Although chemotherapy and radiotherapy are not frequently used, it should be noted that in some cases, postoperative radiotherapy and chemotherapy may be beneficial. The primary treatment approach typically involves the complete surgical removal of the tumor. Here, we discuss the case of our patient whom we successfully treated with extensive resection and followed up with postoperative radiotherapy at our clinic.