Development and Initial Validation of the Macrophage Activation Syndrome/Primary Hemophagocytic Lymphohistiocytosis Score, a Diagnostic Tool that Differentiates Primary Hemophagocytic Lymphohistiocytosis from Macrophage Activation Syndrome

Minoia, Francesca; Bovis, Francesca; Davi, Sergio; Insalaco, Antonella; Lehmberg, Kai; Shenoi, Susan; Weitzman, Sheila; Espada, Graciela; Gao, Yi-Jin; Anton, Jordi; Kitoh, Toshiyuki; Kasapcopur, ÖZGÜR; Sanner, Helga; Merino, Rosa; Astigarraga, Itziar; Alessio, Maria; Jeng, Michael; Chasnyk, Vyacheslav; Nichols, Kim; Zeng Huasong, Zeng; Li, Caifeng; Micalizzi, Concetta; Ruperto, Nicolino; Martini, Alberto; Cron, Randy; Ravelli, Angelo; Horne, AnnaCarin

doi:10.1016/j.jpeds.2017.06.005

Development and Initial Validation of the Macrophage Activation Syndrome/Primary Hemophagocytic Lymphohistiocytosis Score, a Diagnostic Tool that Differentiates Primary Hemophagocytic Lymphohistiocytosis from Macrophage Activation Syndrome

Minoia F., Bovis F., Davi S., Insalaco A., Lehmberg K., Shenoi S., ...More

JOURNAL OF PEDIATRICS, vol.189, pp.72-81, 2017 (SCI-Expanded, Scopus)

Publication Type: Article / Article
Volume: 189
Publication Date: 2017
Doi Number: 10.1016/j.jpeds.2017.06.005
Journal Name: JOURNAL OF PEDIATRICS
Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Page Numbers: pp.72-81
Istanbul University-Cerrahpasa Affiliated: No

Abstract

Objective To develop and validate a diagnostic score that assists in discriminating primary hemophagocytic lymphohistiocytosis (pHLH) from macrophage activation syndrome (MAS) related to systemic juvenile idiopathic arthritis.