Chediak-Higashi syndrome in the intensive care unit

Demirkiran, O; Utku, Tuğhan; Urkmez, S; Dikmen, YALIM

doi:10.1111/j.1460-9592.2004.01257.x

Chediak-Higashi syndrome in the intensive care unit

Demirkiran O., Utku T., Urkmez S., Dikmen Y.

PEDIATRIC ANESTHESIA, cilt.14, sa.8, ss.685-688, 2004 (SCI-Expanded, Scopus)

Yayın Türü: Makale / Tam Makale
Cilt numarası: 14 Sayı: 8
Basım Tarihi: 2004
Doi Numarası: 10.1111/j.1460-9592.2004.01257.x
Dergi Adı: PEDIATRIC ANESTHESIA
Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Sayfa Sayıları: ss.685-688
İstanbul Üniversitesi-Cerrahpaşa Adresli: Hayır

Özet

Chediak-Higashi Syndrome is a rare autosomal recessive disease characterized by recurrent infections, giant cytoplasmic granules and oculocutaneous albinism. We describe the clinical and laboratory findings of a patient with Chediak-Higashi syndrome who was diagnosed and treated in the intensive care unit because of bleeding tendency after surgery.